A rare case of left main coronary artery atresia misdiagnosed as an anomalous left coronary artery from the pulmonary artery and presented as dilated cardiomyopathy

Serdar Basgoze; Bengisu Karakose; Ersin Erek

doi:10.5606/e-cvsi.2023.1503

Cardiovascular Surgery and Interventions 2023, Vol 10, Num 2 Page(s): 134-137

A rare case of left main coronary artery atresia misdiagnosed as an anomalous left coronary artery from the pulmonary artery and presented as dilated cardiomyopathy

Serdar Basgoze¹, Bengisu Karakose², Ersin Erek¹

¹Department of Pediatric Cardiovascular Surgery, Acıbadem University, Istanbul, Türkiye
²Department of Cardiovascular Surgery, Acıbadem University, Faculty of Medicine, Istanbul, Türkiye

Keywords: Bland-White-Garland syndrome, cardiac surgery, congenital heart disease, extracorporeal membrane oxygenation, left main coronary artery disease

Left main coronary artery atresia is one of the rarest congenital anomalies characterized by the absence of the left coronary ostium and the left main trunk. This case report presents an extremely rare left main coronary artery atresia case in a 14-week-old female infant presenting with severe symptoms of dilated cardiomyopathy. The patient underwent surgery after successful weaning from extracorporeal membrane oxygenation (ECMO) support but died because of cranial complications after the second run of ECMO.

DOI : 10.5606/e-cvsi.2023.1503