Cardiovascular Surgery and Interventions 2015, Vol 2, Num 1 Page(s): 013-016
Anesthesia management in left cardiac sympathetic denervation with catecholaminergic polymorphic ventricular tachycardia

Mustafa Şimşek, Türkan Kudsioğlu, Zuhal Aykaç

Department of Anesthesiology and Reanimation, Dr. Siyami Ersek Thoracic and Cardiovascular Surgery Training and Research Hospital, İstanbul, Turkey

Keywords: Anesthesia; catecholaminergic polymorphic ventricular tachycardia; left cardiac sympathetic denervation
Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a rare familial cardiac arrhythmia characterized by RYR2 or CASQ2 gene mutation. This arrhythmia occurs in patients with a structurally normal heart. The syndrome may cause sudden cardiac arrest due to exercise or emotional stress related ventricular fibrillation. Most frequent clinical symptom is syncope. Currently, no definite anesthetic approach is available for the management of these patients. In this article, we report a case of CPVT and discuss anesthetic management.

DOI : 10.5606/e-cvsi.2015.187